The so called Chapel Hill classification defines the different types of vasculitis according to the size of the blood vessels affected.
LARGE VESSEL VASCULITIS (LVV) GCA Giant Cell Arteritis (Arteritis Temporalis) TAK Takayasu Disease MEDIUM VESSEL VASCULITIS (MVV) PAN Polyarteritis Nodosa KD Kawasaki Disease SMALL VESSEL VASCULITIS (SVV) GPA Granulomatosis with Polyangiitis (Wegener's) EGPA Eosinofile Granulomatosis with Polyangiitis MPA Microscopic Polyangiitis (collectively referred to as ANCA Associated SVV) Anti GBM Disease (Good Pasture) IgA vasculitis (Henoch-Schönlein) CV Cryoglobulinemic Vasculitis Anti C1q vasculitis (collectively referred to as Immune Complex SVV) VARIABLE VESSEL VASCULITIS Behçet Disease Cogan's Syndrome SPECIFIC ORGAN VASCULITIS Cubanen leukocytoclastic angiitis (CLA), Cutane Arteritis, Primary CNS vasculitis, Isolated Otitis, and other. |